Of the 60 patients, 40 had DCM with AVB, 12 had DCM with ventricular tachycardia/fibrillation, 6 had DCM with AVB and Emery-Dreifuss muscular dystrophy type 2 (EDMD2), and 2 had AVB plus EDMD2.
英
美
- 60例表现型受到影响的病例中,40例存在扩张型心肌病合并房室传导阻滞,12例存在扩张型心肌病合并室性心动过速/心室颤动,6例存在扩张型心肌病合并房室传导阻滞和2型埃-德二氏肌营养不良(EDMD2),2例出现房室传导阻滞合并2型埃-德二氏肌营养不良。