UAPA diagnosed in childhood usually has unilateral absence of the left pulmonary artery and associated congenital cardiovascular anomaly, while UAPA diagnosed in adult usually has UAPA on the right side without associated congenital anomaly.

• 儿童时期明确诊断的一侧肺动脉缺如多合并有心血管畸形 ,且左肺动脉缺如多见 ,成年人明确诊断的单发一侧肺动脉缺如多为右肺动脉缺如。