This report presents a case of lymphangi-oleiomyomatosis in bilateral lungs, kidneys, liver, retrocrural space and retroperitoneal space without stigmata of tuberous sclerosis.

• 本文报告一例在两侧肺脏、肾脏、肝脏、横隔膜后及后腹腔的弥漫性淋巴血管平滑肌增生症。