In tyrosinase-positive oculocutaneous albinism, melanosomes contain tyrosine, a tyrosinase substrate, but a defect in the tyrosine transport system impairs melanin production.

• 在酪氨酸酶阳性眼皮肤白化,含有黑色素细胞酪氨酸,酪氨酸基板,但缺陷妨碍交通系统的酪氨酸黑色素生产。