Continuous intravenous epoprostenol improves exercise capacity, hemodynamics, and survival in IPAH and is the preferred treatment option for the most critically ill patients.

• 持续静脉输注依前列醇以提高运动能力，血流动力学，还可提高IPAH患者的生存期，而对于急危重病人依前列醇则是首选的治疗方法。